Alagille Syndrome: A case report of a rare oral and multisystem manifestation
University of Mohammed V, Faculty of dentistry, Departement of Pediatric Dentistry, Rabat-MOROCCO
Case Study
World Journal of Advanced Research and Reviews, 2022, 13(01), 317–321
Article DOI: 10.30574/wjarr.2022.13.1.0012
Publication history:
Received on 05 December 2021; revised on 07 January 2022; accepted on 09 January 2022
Abstract:
Alagille syndrome is an inherited multisystem disorder of autosomal dominant transmission. Its prevalence is estimated at 1 per 70,000 to 100,000 live births. We report the case of a young patient suffering from Alagille syndrome who consulted the center of diagnosis and dental treatment of Rabat - MOROCCO (CCTD). The general manifestations are facial dysmorphia, hepatic, cardiac, and ocular disorders. Hepatic cholestasis causes oral repercussions such as a yellow oral mucosa, hypomineralization of the teeth, and a high tendency to dental caries.
The management of such a patient requires the knowledge of the general health of the patient, therefore collaboration with the attending physicians, the establishment of rigorous oral hygiene, personalized prophylaxis with a consequent contribution of fluorine.
Keywords:
Alagille Syndrome; Oral Manifestations; Hypomineralization of the enamel; Oral Care
Full text article in PDF:
Copyright information:
Copyright © 2022 Author(s) retain the copyright of this article. This article is published under the terms of the Creative Commons Attribution Liscense 4.0