Dermatofibrosarcoma protuberans of the breast: A case report of a rare breast tumour

CD Emegoakor 1, HC Nzeako 1, MI Nwosu 1, ME Chiemeka 2, * and FE Menkiti 2

1 Department of Surgery, Nnamdi Azikiwe University Teaching Hospital, Nnewi.
2 Department of Anatomic Pathology and Forensic Medicine, Nnamdi Azikiwe University Teaching Hospital, Nnewi.
 
Case Study
World Journal of Advanced Research and Reviews, 2021, 11(02), 112–116
Article DOI: 10.30574/wjarr.2021.11.2.0317
 
Publication history: 
Received on 05 June 2021; revised on 27 July 2021; accepted on 29 July 2021
 
Abstract: 
Introduction: Dermatofibrosarcoma protuberans (DFSP) is an intermediate and slow-growing sarcoma, arising most commonly in the trunk and extremities and rarely in the breast. It may be recurrent, but metastasis is rare. Excision with good resection margins reduces the rate of recurrence.
Case Presentation: A 28-year-old lady presented with a painless lump in the left breast of 16 years duration. Examination revealed an ulcerated firm mass, well defined, with perilesional nodules on the skin of the breast. Wedge biopsy favoured Borderline Phylloides Tumour over DFSP. Patient was offered mastectomy and the histology of the specimen confirmed Fibrosarcomatous DFSP.
Conclusion: This stresses the importance of histology in diagnosing a rare breast tumour. This is very important because it may show similar appearance to other benign and malignant breast lesions, which makes clear the role of pathological investigation to make a definitive diagnosis.
 
Keywords: 
Breast; Dermatofibrosarcoma Protuberans; Mesenchymal Tumour; Fibrosarcomatous DFSP
 
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