Deformation of Sprengel in children: About three cases and review of the literature

Bienvenu Jean Celien Okouango 1, *, Wilhem Donald Aloumba Gilius 2, Chancy Rosine Mady Goma 3, Mohamed Fargouch 1, Driss Bennouna 1, 4 and Mustapha Fadili 1, 4

1 Department of Orthopedic Traumatology, Wing 4, University Center Hospital Ibn Rochd, Casablanca, Morocco.
2 Department of Radiology, Abderrahim Harouchi Mother-Child Hospital, University Center Hospital Ibn Rochd, Casablanca, Morocco.
3 Department of Pediatric surgery, Abderrahim Harouchi Mother-Child Hospital , University Center Hospital Ibn Rochd , Casablanca, Morocco
4 Faculty of Medicine and Pharmacy of Casablanca, Hassan II University, Morocco.
 
Case Study
World Journal of Advanced Research and Reviews, 2024, 22(03), 669–673
Article DOI: 10.30574/wjarr.2024.22.3.1761
 
Publication history: 
Received on 01 May 2024; revised on 08 June 2024; accepted on 11 June 2024
 
Abstract: 
We report three cases of congenitally elevated scapula or Sprengel deformity diagnosed and followed in our hospital. This very rare congenital deformation of the shoulder girdle is characterized by more or less deformed and abnormally high shoulder blades. It is often found in young children, causing functional and aesthetic problems. When surgery is indicated, imaging examinations are recommended to diagnose structures from the scapula to the cervical spine, ossified (omo vertebrae) or non-ossified (fibrous and/or cartilaginous junctions). Ultrasound is readily available and, above all, easy to perform for young children. The CT scan is essential to look for an omovertebra and associated vertebral anomalies. Magnetic resonance imaging is useful for evaluating possible fibrous and/or cartilaginous components.
 
Keywords: 
Deformation; Malformation; Sprengel; Elevation; Scapula
 
Full text article in PDF: 
Share this